Elena Cantoni1, Giovanni Sighinolfi1, Magali Jane Rochat1, Micaela Mitolo1,2, Mainieri Greta1,3, Greta Venturi1, Claudio Bianchini3, Lorenzo Cirignotta4, Fiorina Bartiromo1, Gianfranco Vornetti1,3, David Neil Manners1,5, Federica Provini1,3, Raffaele Lodi1,3, and Caterina Tonon1,3
1IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy, 2Department of Medicine and Surgery, University of Parma, IT, Parma, Italy, 3Department of Biomedical and NeuroMotor Sciences, University of Bologna, IT, Bologna, Italy, 4Department of Medical and Surgical Sciences, University of Bologna, IT, Bologna, Italy, 5Department for Life Quality Studies, University of Bologna, IT, Bologna, Italy
Synopsis
Keywords: Other Neurodegeneration, Brain, Disorder of Arousal, Biomarkers, Brain Connectivity, fMRI (resting state), Functional connectivity, Metabolism, Neuroscience, Spectroscopy
Motivation: A comprehensive framework for the characterization of Disorders of Arousal (DoA) in adulthood is lacking, and the brain metabolic and functional mechanisms underlying this disorder are still unknown.
Goal(s): To fill this gap, we aimed to quantitatively investigate the cingulate cortex in DoA through advanced brain MRI, combined with thorough neuropsychological evaluations.
Approach: We collected and compared resting-state, 1H-MRS and clinical data from adult patients diagnosed with DoA and a matched group of healthy controls.
Results: We identified metabolic and functional alterations in regions involving the limbic system and changes in the connectivity of the sensorimotor network crucial for understanding the pathology.
Impact: Through a combined MR imaging investigation
and psychological assessments, we extracted results in the form of brain
metabolic and functional quantitative markers that advance our knowledge on the
brain alterations underlying Disorders of Arousal.
Introduction
Disorders of Arousal (DoA) are parasomnias characterized by involuntary
motor and emotional behaviors arising out of non-REM sleep. Psychological
distress could be a precipitating factor although the relationship with DoA
episodes is controversial1. In this study of adult DoA patients, we investigated
both brain functional networks using resting
state fMRI techniques, and metabolism in the cingulate cortex (CC), a key region in emotion and
behavior regulation2, by
means of 1H-MRS.Methods
Fifteen adult patients with DoA (8F; 26.9±7.8yo, range 19-47yo) and 15
healthy controls (HC, 7F; 25.6±2.7yo, 21-30yo) were recruited. The same MRI and
neuropsychological assessment protocol was administered to each participant.
The MRI protocol (Siemens MAGNETOM Skyra 3T scanner with a head–neck
high-density 64 channels array coil) included a 1-mm isotropic 3D
MPRAGE-T1-weighted sequence, a resting-state fMRI (rs-fMRI) sequence and two
single-voxel 1H-MRS PRESS sequences (TR/TE=2000/30,128
averages, 8 ml volume) within the anterior (ACC) and posterior cingulate
cortices (PCC) (Figure 1a).
FreeSurfer 5.3 was used to extract volumetric data
in the sub-parcellations of the CC defined by the Destrieux atlas3(Figure
1b). Metabolite content was quantified with LCModel 6.3: N-acetyl-aspartate (NAA),
choline (Cho), myo-Inositol (mI), glutamate (Glu), glutamine (Gln), and
glutamate complex (Glx) related to creatine (Cr) or mI as internal reference
were measured. The rs-fMR images were analysed via FSL4 tools using
Seed-Based Analysis (SBA) of the FreeSurfer sub-parcellation of the CC and
Independent Component Analysis (ICA) to study resting-state networks involving
this region.
The normality of sample distributions was tested with Shapiro-Wilk
test. Student’s t-test or Mann-Whitney tests were executed for
neuropsychological assessments, ANCOVA was performed for morphometric data
(covariates: total intracranial volume), and to compare metabolite ratios (covariates:
sex, age). Dual regression coupled with general linear model was used to
compare rs-fMRI maps (covariates: sex, age). Pearson/Spearman’s partial
correlations, regressing out age, sex and education, were calculated between
clinical scales and functional connectivity and spectroscopic results.
Statistical significance was set at p<0.05 after false discovery rate or
family-wise error (for rs-fMRI) correction for multiple comparisons.Results
On
neuropsychological testing, DoA patients displayed increased stress levels
(P=0.03), a higher overall score of emotion dysregulation (P=0.04) and a borderline
significance on some subitems of childhood trauma questionnaire (P=0.05).
The CC sub-parcellation was not significantly different between DoA and
HC.
Patient metabolic profiles in the PCC (Figure 2) were characterized by a
significant decrease of the Gln (P-adjusted<0.001), but not Glx. In the ACC
no metabolic differences emerged. In the patient group, spectroscopic data did
not correlate with clinical scales after correction for multiple comparisons.
Considering the entire sample (DoA+HC), Glx significantly correlated with the
DERS Impulse Control Difficulties scale (P-adjusted=0.008).
Using ICA, significantly increased connectivity between the sensory-motor network
(SMN) with opercular cortex, praecuneus, occipital pole and lingual gyrus was
found in patients (P-adjusted<0.05, Figure 3a). Moreover, lower PCC
connectivity was found in extensive regions (Figure 3b), including motor areas,
ACC, putamen, hippocampus and thalamus (P-adjusted<0.05). Among patients, no
correlation with clinical data survived multiple comparison. In the full
sample, SMN connectivity correlated with emotion regulation, sleep and
depression scales (P-adjusted<0.04); posterior cingulate connectivity
correlated with depression scores (P-adjusted<0.05).Discussion
Cingulate cortex represents a key structure in
the deep complexity of limbic system5, PCC appears as one of the
most important multi-sensorial integration areas, involved in arousal and
awareness processes. Our study showed metabolic alterations of PCC through 1H-MRS
and disrupted functional connectivity of PCC and SMN. As glutamine is involved
in excitatory and inhibitory activity, Gln deficiency in patients might account
for functional alterations of stress control and, overall, an unbalanced
emotion regulation. The metabolic alterations in PCC, not previously
investigated by means of spectroscopy techniques, are consistent with the
connectivity changes of this central hub, as SBA showed decreased connectivity
of left dorsal PCC with several cortical and subcortical areas. The increased
connectivity of SMN with frontal operculum and other regions of interest in
resting-state condition may be related to a cortical “facilitation” of motor
circuits, especially under unaware conditions. No volumetric alterations
previously found in PCC6, and ACC
metabolic variations have been confirmed in this study, possibly due to the
small study sample and CC parcellation.Conclusions
New findings
in DoA mechanisms, obtained
combining MRI data and specific clinical assessments, revealed complex
processes underlying arousal and awareness. The ACC normal
metabolic profile might be useful to discriminate between subjects with
parasomnias and those with similar motor signs such as frontal nocturnal
epilepsy7. The increased connectivity of the SMN and the crucial
role of the PCC in emotional dysregulation8 contribute to characterize
DoA patients’ pathophysiology. Acknowledgements
No acknowledgement found.References
- Castelnovo,
Anna, et al. "Behavioural and emotional profiles of children and
adolescents with disorders of arousal." Journal of
sleep research 30.1 (2021): e13188.
- Ramm, Markus, et al. "Increased behavioral
inhibition trait and negative stress coping in non–rapid eye movement
parasomnias." Journal of Clinical Sleep
Medicine 16.10 (2020): 1737-1744.
- Destrieux, Christophe, et al. "Automatic
parcellation of human cortical gyri and sulci using standard anatomical
nomenclature." Neuroimage 53.1 (2010): 1-15.
- Jenkinson, Mark, et al.
"Fsl." Neuroimage 62.2 (2012): 782-790.
- Vogt, Brent A. "The cingulate cortex in neurologic diseases:
history, structure, overview." Handbook of Clinical Neurology 166
(2019): 3-21.
- Heidbreder,
Anna, et al. "Gray matter abnormalities of the dorsal posterior cingulate
in sleep walking." Sleep Medicine 36
(2017): 152-155.
- Naldi,
Ilaria, et al. "Proton MR spectroscopy in patients with sleep-related
hypermotor epilepsy (SHE): evidence of altered cingulate cortex
metabolism." Sleep 40.9 (2017): zsx115.
- Gibbs,
Steve A., et al. "Sleep-related epileptic behaviors and
non-REM-related parasomnias: insights from stereo-EEG." Sleep Medicine Reviews 25 (2016): 4-20.