Lena V. Gast1, Teresa Gerhalter1, Matthias Türk2, Alper Sapli1, Rafael Heiss1, Claudius S. Mathy1, Pierre-Yves Baudin3, Benjamin Marty3, Michael Uder1, and Armin M. Nagel1,4
1Institute of Radiology,University Hospital Erlangen, Friedrich-Alexander-Universität Erlangen-Nürnberg (FAU), Erlangen, Germany, 2Department of Neurology, Friedrich-Alexander-Universität Erlangen-Nürnberg (FAU), Erlangen, Germany, 3NMR Laboratory, Neuromuscular Investigation Center, Institute of Myology, Paris, France, 4Division of Medical Physics in Radiology, German Cancer Research Center (DKFZ), Heidelberg, Germany
Synopsis
Keywords: Muscle, Muscle
Motivation: Combined 23Na/39K MRI at 7T can highlight ion disturbances related to patho-physiological processes within dystrophic muscle tissue. However, quantification of the apparent tissue potassium concentration (aTPC) using 39K MRI is challenging due to low signal-to-noise and rapid signal decay.
Goal(s): Here, we investigated the feasibility of quantitative 39K MRI in dystrophic muscle tissue.
Approach: The lower leg of 14 FSHD patients and 11 healthy controls was examined using 39K/23Na and 1H MRI at 7T.
Results: We found a strongly reduced aTPC in fat infiltrated muscles. After correction for reduced potassium concentration in fat, aTPC values in dystrophic muscles were similar to healthy muscles.
Impact: Potassium
concentration in fatty tissue is strongly reduced compared to healthy skeletal
muscle tissue. This has to be considered when investigating and interpreting aTPC
values measured with 39K MRI in fat-replaced skeletal muscle tissue.
Introduction
Sodium and potassium
ions play an essential role in the excitability of muscle cells due to their
concentration gradients between the intracellular and extracellular space,
which is maintained by the Na+-K+-ATPase. Various
diseases, including muscular dystrophies, have been reported to alter the
ATPase activity1. Sodium (23Na) MRI has already been
successfully applied to detect altered apparent tissue sodium concentrations
(aTSC) in muscle tissue of muscular dystrophy patients such as Facio-scapulo-humeral muscular dystrophy
(FSHD)2. A combination with 39K MRI could
provide a comprehensive insight into the ion homeostasis of dystrophic skeletal
muscle tissue. However, 39K MRI suffers from a very low
signal-to-noise ratio and a very rapid biexponential signal decay (T2short* = 1.2 ms, T2long*
= 8.1 ms in muscle
tissue3), making quantification of the apparent tissue
potassium concentration (aTPC) challenging. So far, quantitative 39K MRI has
mostly been applied to healthy skeletal muscle tissue3-5.
Here, we examined the lower leg of FSHD patients using quantitative 39K MRI together with 23Na
and 1H MRI at 7T. We
investigated the impact of fat infiltration on the measured aTPC, and compared the resulting aTPC/aTSC values to healthy
muscle tissue.Methods
14
patients (6f/8m, mean age 47.7±14.0 years) with genetically proven FSHD and 11
healthy controls (4f/6m, mean age 45.4±13.5 years) were examined using a whole-body
7T MRI system (Magnetom Terra, Siemens Healthcare GmbH). 23Na/39K
MRI data was acquired using a double-resonant 23Na/39K birdcage RF coil (Rapid Biomedical GmbH) and a 3D density-adapted radial readout scheme with cubic field-of-view (parameters see Table 1). During examinations, the leg was lying on a five-compartment
reference container filled with different combinations of NaCl and K2HPO4
solution. In addition, T1
weighted water-excitation, and multi-echo spin-echo (MESE) 1H MRI
data were acquired using a 28-channel 1H knee RF coil.
Based
on the T1 weighted 1H images, seven individual muscle
regions and subcutaneous adipose tissue were segmented6. Using these
segmentation masks, a region-based partial volume correction (PVC) was applied
to the 39K/23Na MRI data4. Furthermore, a
correction for relaxation biases was applied. aTPC/ aTSC values were then
calculated by calibrating the 39K/23Na MRI signals
based on the reference compartments using a linear regression. Median water T2
relaxation times (T2w) and fat fraction (FF) values were extracted
from the MESE 1H MRI data using an extended phase-graph (EPG) fit7.Results
Figure 1 shows 39K/23Na MR images after correction of relaxation effects together with T1 weighted 1H images and T2w
maps. 39K MRI was highly sensitive to fat infiltration and clearly depicted
the muscle degeneration. Particularly, even in regions with normally appearing or increased 23Na MR signal, a strongly reduced 39K
MRI signal was observed.
Figure 2 shows the dependence of
the measured aTSC and aTPC values after PVC on the FF derived from the EPG fit.
While aTSC values were increased for medium FFs and decreased for very high
FFs, aTPC values strongly decreased with FF already at medium FF values. For
very high FFs (> 80%), the mean aTPC value was close to zero (4.8 ± 2.9 mM).
A
comparison between the quantitative values measured in FSHD patients and
healthy controls before and after fat correction (up to a FF of 60%) is shown
in Figure 3. FF values were
significantly increased in GM and TA muscles in FSHD patients compared to
controls (p=0.046/0.008, Wilcoxon rank-sum test), while T2w values
remained at a normal level. Fat corrected aTSC values were significantly
increased in TA and EDL (p=0.033/0.010). After fat correction, aTPC values were in a
similar range as corresponding values in healthy muscle tissue, and no significant differences were found. Discussion
Due
to the low potassium concentration in fat, aTPC showed a
stronger dependence on fat infiltration than aTSC. To assess the
aTPC in the remaining muscle tissue, a fat correction was
performed analogously to the correction of aTSC as reported before2,8. For this correction, we used
FF values resulting from the EPG T2w fit as no optimized Dixon-based fat-water separation
was available at 7T. However, FF values resulting from EPG T2w
fit might be biased, especially in regions of strong edema and high fat
infiltration. As quantitative 1H MRI approaches are generally more
challenging at ultra-high field (e.g. due to inhomogeneities in B0/B1), it might be advantageous to combine 39K/23Na MRI at 7T with more stable and reliable 1H
MRI sequences for skeletal muscles at 3T.Conclusion
Quantitative
combined 39K/23Na MRI of dystrophic skeletal muscles
is feasible at 7T, however, it requires the correction of reduced ion
concentrations in fatty tissue to assess changes in remaining muscle tissue.Acknowledgements
No acknowledgement found.References
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