Dean Tran1, Phillip DiGiacomo1, Marios Georgiadis1, Nicholas Edwards2, Sharon Bone2, Donald Born3, Samuel Webb2, and Michael Zeineh1
1Department of Radiology, Stanford University, Stanford, CA, United States, 2Stanford Synchrotron Radiation Lightsource, SLAC National Accelerator Laboratory, Menlo Park, CA, United States, 3Department of Pathology, Stanford University, Stanford, CA, United States
Synopsis
Keywords: Alzheimer's Disease, Alzheimer's Disease, X-ray microscopy
Recent studies suggest that iron and neuroinflammation are key
components of AD pathology. Specifically, ferrous Fe
2+ can cause
oxidative stress, a possible a mechanistic link to disease progression. Correlative
ex vivo MRI can detect iron-containing microglia in AD hippocampi, but
whether this iron is ferrous is unknown. Synchrotron X-ray absorption near edge
spectroscopy (XANES) can quantify iron oxidation state in frozen human brain samples.
However, tissue thawing during the long scans might affect the oxidation state.
Here, we implement the necessary hardware to interrogate that question and
present preliminary evidence that, as specimens thaw, less redox-active ferrous
iron is measured.
Introduction
Alzheimer’s disease (AD)
has primarily been characterized by the accumulation of β-amyloid (Aβ) in
plaques and phosphorylated tau in neurofibrillary tangles, although there is
evidence that these markers are not solely responsible for
neurodegeneration. Notably, there exists an abundance of evidence supporting
the presence of iron accumulation in AD, as reviewed in Tran et al. 20221,
among others. For example, MRI has been used alongside coregistered histology
to show iron-containing activated microglia within the hippocampus in advanced
AD but not in age-matched controls2. However, the specific role that
iron plays in the mechanisms of AD neurodegeneration is presently unknown.
One hypothesis is that
the conversion of ferric (Fe3+) to ferrous (Fe2+) iron in
the AD brain leads to production of free radicals via the Fenton reaction, which,
in turn, causes oxidative damage to neurons3,4. For this reason, an
outstanding question to understand the role of iron in AD pathology is to
determine the relative oxidation state of iron in health and disease.
To interrogate this
question, we have aimed to perform synchrotron
X-ray fluorescence imaging (XFI) to map iron deposition5,6 and X-ray
absorption near edge spectroscopy (XANES) to quantify oxidation state of
specific iron deposits in human brain tissue7,8 (from AD subjects
and age-matched healthy control) in collaboration with colleagues at the SLAC
National Accelerator Laboratory (SLAC). X-ray microscopy is uniquely suited to
identify iron in the same scale as specimen MRI and characterize the oxidation
state with absorption spectroscopy. To minimize effects of formalin fixation
and capture iron in its most biologically relevant state, we generally use unfixed, frozen specimens
for these experiments, while performing MRI on the contralateral formalin-fixed
hippocampus, to enable correlation of X-ray based measures of iron to
quantitative MRI and facilitate clinical translation (Figure 1). However, during the hours-long imaging, slides quickly thaw, and the
effect of thawing on iron speciation in situ is unknown.
Recently, we have built and implemented a frozen chamber for the SLAC beam-line.
The current work aimed to acquire high-resolution mapping and quantification of
iron oxidation state in human brain tissue in a maintained frozen state, and to
assess whether thawing
affects XANES measurement of iron’s oxidation state in the same tissue.Methods
Frozen hippocampi were
acquired from AD and control subjects from the Stanford Neuropathology Core
affiliated with the Stanford Alzheimer’s Disease Research Center. Samples were
frozen-sectioned at 30 μm slice-thickness. Two hippocampi were scanned for
these experiments.
XFI and XANES were
performed at using a cryo-chamber at beamline 2-3, which has a beam size of 3μm.
XFI was obtained at up to 5μm in-plane resolution to guide selection of 6
individual iron-rich deposits for each specimen, while kept in the cryo-chamber
at -20o C.
XANES spectra were acquired on each deposit while frozen at -20o C (four
averages per deposit), and subsequently reacquired on the exact same deposits
at room temperature after allowing tissue to thaw, allowing us to directly
compare the effects of thawing on XANES spectra. Additional adjacent deposits
were scanned at room temperature to control for potential effects of the X-ray
beam itself.
Visualization and
averaging of individual spectra acquired for each specimen was performed using
MicroTool Kit. These averaged spectra were then energy calibrated using the
spectra from a standard iron foil. An in-house MATLAB script performed
background subtraction and normalization by linearly fitting the pre-edge (up
to 7105 eV) and the post-edge (beyond 7200 eV) to normalize the background to roughly
zero in the pre-edge and generate a unit-step edge with a roughly constant
post-edge of one. To obtain an estimate of the relative proportion of different
iron species within individual deposits, reference X-ray absorption spectra
from standards of ferrihydrite (Fe3+) and FeSO4 (Fe2+),
each of which had undergone the same background removal process, were used to
fit the measured iron L2,3-edge X-ray absorption spectra from each
deposit, using a non-linear least-squares fitting procedure.Results
We found that, on average, thawed iron deposits in both scanned
specimens exhibited a slight rightward shift in the normalized XANES spectra
compared to the same deposits scanned while frozen (Figure 2),
suggesting a decrease in measured Fe2+ and an increase in Fe3+ caused
by thawing. Fitting the X-ray spectra to standards estimated the Fe3+/Fe2+
composition, which confirmed a quantitative increase in Fe3+ composition,
accompanied by decreases of Fe2+, across specimens and deposits (Figure
3).Discussion and Conclusion
We have implemented a
novel cryochamber hardware setup to interrogate the effects of freezing and
thawing on XANES-measured oxidation state of iron in human brain tissue. Our
preliminary results suggest a possible change in iron speciation, with an
increase in Fe3+ following thawing. This could be due to the
increase of oxygen reactivity upon thawing, driving iron oxidation. This result suggests that measurements under a thawed state will alter
iron oxidation and underestimate the amount of Fe2+, which can also
affect MRI measurements9. Our ongoing work will collect more data
from additional specimens, using this method to investigate differences in iron
oxidation state in biological brain specimens.Acknowledgements
No acknowledgement found.References
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