Ho-Fung Chan1, Guilhem J Collier1, Laurie J Smith1, Alberto M Biancardi1, Jody Bray1, Helen Marshall1, Paul J.C Hughes1, Madhwesha Rao1, Graham Norquay1, Andrew J Swift1, Kylie Hart2,3, Michael Cousins2,3, Sailesh Kotecha2,3, and Jim M Wild1
1Infection, Immunity and Cardiovascular Disease, University of Sheffield, Sheffield, United Kingdom, 2Child Health, Cardiff University School of Medicine, Cardiff, United Kingdom, 3Neonatal Unit, Cardiff and Vale University Health Board, Cardiff, United Kingdom
Synopsis
Ventilation defects
and increased alveolar heterogeneity have been observed previously with 129Xe
MRI in preterm-born children. We hypothesised that reduced gas exchange in
preterm-born children could be measured with dissolved 129Xe whole
lung spectroscopy. The ratio of red blood cells (RBC) to tissue/plasma
(TP) signals (RBC/TP) was significantly elevated in the lungs of 34
preterm-born children compared with 16 term-born children. This trend
was unexpected and we hypothesise that in preterm-born children a reduced
number of alveolar septa due to birth at an early stage of lung development can
lead to decreased TP signal and thus increased RBC/TP ratio.
Introduction
Babies born preterm (<37 weeks’
gestation) are at risk of decreased lung function in childhood and beyond due
to a combination of birth at an early stage of lung development and exposure to
antenatal and postnatal factors that can lead to the development of
bronchopulmonary dysplasia (BPD)1. Hyperpolarised 129Xe MRI is safe
and well-tolerated in paediatric subjects and could play a role in phenotyping
different lung diseases resulting from preterm-birth. Previously, ventilation
defects and increased alveolar heterogeneity were demonstrated in the lungs of preterm-born
children with 129Xe MRI2. However, the
sensitivity of dissolved 129Xe MRI to gas transfer limitations has
not yet been explored in these children. Transfer factor of the lung for carbon
monoxide (TLCO) has been demonstrated to be lower in
preterm-born children compared with healthy term-born controls3,4, and we
hypothesised that similar differences could be measured with hyperpolarised dissolved
129Xe spectroscopy.Methods
50 children aged 9-13 years, including 34
preterm-born (≤34 weeks’ gestation) and 16 term-born controls, were imaged with
hyperpolarised 129Xe MRI on a 1.5T GE HDx scanner using a
transmit/receive quadrature vest coil as part of the Respiratory Health
Outcomes in Neonates study (RHiNO, EudraCT: 2015-003712-20). Dissolved 129Xe
whole lung spectroscopy was acquired after inhalation of a gas mixture of 129Xe and N2 from functional residual capacity (FRC) and a 15
second breath-hold. Gas mixture volume and 129Xe doses5 (300-500 mL)
were adjusted according to the subjects’ heights to account for differences in
lung volume and 129Xe concentration. Sequence parameters were: BW=8
kHz, 512 pts, 200 averages, TR=74 ms, and 22° flip angle. A double Lorentzian
fit of the whole lung spectroscopy data in the frequency domain was performed6 to
derive T2* values of the tissue/plasma (TP) and red blood cell (RBC)
peaks, and the ratio of RBC to TP signals (RBC/TP). A single Lorentzian fit was
also performed on the gas peak to determine the reference gas frequency to
calculate the RBC and TP frequency shifts.
The RHiNO study groupings were
defined as: preterm with low lung function (PTLow, percent predicted
FEV1≤85%), preterm with normal lung function (PTNorm, %FEV1>85%)
and term-born controls. The 34 preterm-born children were also grouped based
upon their diagnosis of BPD (supplemental oxygen dependency at 28 days of age
in the neonatal period) (PTBPD) or into preterm without BPD (PTnBPD).
Kruskal-Wallis tests with post-hoc Dunn’s correction for multiple comparisons were
performed to assess differences across the stratified %FEV1 or BPD
groups against the term-born controls for all 129Xe spectroscopy
metrics and subject demographics. Non-parametric Spearman’s correlation was
used to assess correlations between 129Xe spectroscopy metrics and
demographics across all subjects.Results and Discussion
Subject
demographics and 129Xe spectroscopy metrics are shown in Table 1. 129Xe
RBC/TP in the healthy term-born children (mean age=11yrs; RBC/TP=0.42) was
smaller than the reported ratio in healthy adults (mean age=41yrs; RBC/TP=0.56)
using the same spectroscopy sequence (Figure 1)7. The mechanism
behind this trend is likely to be due to increased haematocrit in adults
resulting in increased 129Xe RBC signal8. This trend in
RBC/TP also matches the changes in predicted TLCO with age where TLCO
increases throughout childhood and slowly declines with advancing age in adults9.
129Xe RBC/TP
was significantly different for both %FEV1 (P=0.002) and BPD
(P<0.001) stratified groups (Figure 2). No significant differences were observed
between %FEV1 and BPD groups for the other 129Xe
spectroscopy metrics. Significantly increased RBC/TP ratio was observed for preterm
groups compared with term-born controls: PTLow (P=0.008), PTNorm
(P=0.007), PTnBPD (P<0.001). Differences in RBC/TP between term-born
and preterm-born children suggests that these differences are due to underlying
preterm birth regardless of low FEV1 and/or BPD diagnosis. This is
further supported by significant correlations of gestational age (P=0.014,
r=0.344) and birthweight with RBC/TP (P=0.016, r=0.340) (Figure 3).
The increased 129Xe RBC/TP observed
for preterm-born children, with respect to term-born controls, appears to be
directly opposite to the expectation of decreased RBC/TP due to reduced gas
transfer as a result of immature lungs having simplified alveoli geometry and
reduced surface area1,3,4. While 129Xe
RBC/TP has been shown to strongly correlate with gas transfer or exchange in a range
of pulmonary diseases6,7,10, this
biomarker is highly representative of the alveolar-capillary gas exchange
surface. We hypothesise that in these preterm-born children the increased 129Xe
RBC/TP is due to a decreased TP component resulting from simplified alveolar
geometry with reduced alveolar septation1. Fewer alveolar septa leads to
regions of enlarged alveoli and increased alveolar heterogeneity has been
detected previously with 129Xe diffusion-weighted MRI2. A negative correlation between 129Xe
mean alveolar dimension (LmD) and TP T2*, but no
correlation between LmD and RBC T2* (Figure 4), further
supports the fewer alveolar septa hypothesis by demonstrating that heterogeneity
in the TP component (low TP T2*) is related to increased alveolar
dimensions. Conclusion
129Xe RBC/TP,
derived from dissolved 129Xe spectroscopy, was significantly
elevated in 34 preterm-born children compared with 16 term-born controls. We
hypothesise that in preterm-born children simplification and reduced number of alveolar
septa can result in decreased TP signal and thus increased RBC/TP ratio. Acknowledgements
This work was supported by the Medical Research Council (MR/M008894/1 and MR/M022552/1)
and National Institute for Health Research grant (NIHR-RP-R3-12-027). References
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