Alecio Lombardi1,2, Jonathan Wong1,2, Rachel High1,2, Ya-Jun Ma2, Adam Searleman2, Saeed Jerban2, Qingbo Tang1,2, Jiang Du1,2, Patrick Frost3,4, and Eric Y. Chang1,2
1Radiology Service, Veterans Affairs San Diego Healthcare System, San Diego, CA, United States, 2Radiology, University of California, San Diego, CA, United States, 3Greater Los Angeles Veteran Administration Healthcare System, Los Angeles, CA, United States, 4University of California, Los Angeles, CA, United States
Synopsis
Multiple myeloma (MM)
is a malignant plasma cell disease. Adaptive
responses to hypoxia may be an essential element in its progression. The purpose of this study was to determine the feasibility of
acidoCEST MRI for pHe measurement on a mouse
model of MM with comparison with GLUT1 staining.
Introduction
Multiple myeloma (MM), the most frequent cancer to
involve the skeleton, is an incurable disease of malignant plasma cells
accumulated in the bone marrow (BM) 1. Despite newer treatments 3, patients with
refractory and relapsing disease still have a poor outcome 4. Previous studies point to hypoxia’s
adaptive responses as an essential element in MM progression 5 and drug
resistance 6.
Tumors such as MM tend to favor glycolysis even in aerobic
conditions (known as the Warburg effect) 7. The Warburg effect leads to an increased metabolic rate, glucose transporters, lactic acid, and carbonic acid, resulting in a decrease in the extracellular pH (pHe) 8. The degree of hypoxia-responsive metabolic changes
and their corresponding pHe decrease depends upon the upregulation of glucose
transporters (GLUTs) to provide increased glucose uptake, making it an interesting biomarker of hypoxia and tumor cells 9.
AcidoCEST MRI, on the other hand, is a technique that uses the contrast agent iopamidol to induce chemical exchange saturation transfer (CEST) effect in water molecules, altering the MRI signal (Figures 1 and 2). The CEST effect is pH-dependent, thus allowing indirect measurement of the extracellular pH . The high spatial resolution may prove invaluable since MM displays
enormous inter-and intra-tumoral heterogeneity, which has significant
consequences for MM patients' clinical management and outcome 10. This study aimed to determine the feasibility of
acidoCEST MRI for in vivo pHe measurement using an orthotopic mouse model of MM
compared with GLUT1 immunofluorescence staining as a reference standard.
Methods
Orthotopic
BM engrafted MM xenografts were established in NSG/NOD mice using the human 8226 myeloma cell line. Tumor development in the
BM was monitored with luciferase activity using a bioluminescent imaging system.
AcidoCEST MRI was performed on a Bruker BioSpec 7T system approximately six weeks after intravenous challenge, before and after intravenous administration of iopamidol. BM pHe
values were generated via fitting the CEST spectrum with the Bloch-McConnell
equations. After sacrificing, osseous structures were imaged with confirmation
of lesions using a µCT scanner. Samples were decalcified, sectioned, and immunostained
for GLUT1 expression. Pearson’s correlation was used to assess the relationship
between MRI pHe and [H3O] versus GLUT1 expression.Results and Discussion
The spine was selected for CEST-FISP imaging in 7 cases, the lower
extremity in 2 cases, and the bony pelvis in 1 case (Figures 3 and 4). GLUT1 signal showed strong expression and immunostaining in the bone marrow affected by tumor cells, with varying levels of signal intensity. A strong negative correlation was seen between MRI pHe versus GLUT1 expression
(r = -0.75, p < 0.001) (Figure 5). After transformation of pH to [H3O], a strong
positive correlation between [H3O] and GLUT1 expression was seen (r = 0.8, p
< 0.001) (Figure 6).
Ideally, acidoCEST MRI could complement 18F-FDG PET and other
molecular imaging modalities to access tumor metabolism. The total metabolic activity of cancer cells may be better assessed with
pHe measurements than with established metabolic markers, so it should be
investigated as a superior clinical proxy 11,12,13,14. Conclusion
In
conclusion, acidoCEST MRI can measure the extracellular pH of bone marrow
affected by multiple myeloma. In this MM orthotopic mouse model, pHe measured
by acidoCEST MRI showed strong correlations with the metabolic phenotype of BM
tumor assessed by immunofluorescent histological assessment of GLUT1
overexpression.Acknowledgements
The authors acknowledge grant support from the NIH (R01
AR062581, R01 AR068987), Veterans Affairs (I01RX002604 and I01CX001388), and GE
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