Ben A Duffy1, Julia Pia Simon1, Yan Li2, Arthur W Toga1, Wolfgang G Muhlhofer3, Robert C Knowlton2, and Hosung Kim1
1USC Stevens Neuroimaging and Informatics Institute, University of Southern California, Los Angeles, CA, United States, 2UCSF Weill Institute for Neurosciences, San Francisco, CA, United States, 3University of Alabama at Birmingham, Birmingham, AL, United States
Synopsis
The pathophysiology of
MRI-negative temporal lobe epilepsy is not well understood. Here, we used a surface-based
approach for investigating metabolic changes in the subregions of mesiotemporal
structures for MRI-negative TLE patients. We found significant hypometabolism
in the anterior to the intermediate hippocampus, the intermediate entorhinal
cortex and the centro-medial and laterobasal amygdala. In patients with poor
outcome, metabolism tended to be more interhemispherically symmetric in all three
regions compared to those with good outcome, which suggests a more complicated
seizure origin in this subtype of the disorder.
Introduction
The pathophysiology of MRI-negative
temporal lobe epilepsy (TLE) is not well understood. In addition, it represents
a challenge for surgical planning due to the lack of identifiable lesions and its
association with poorer surgical outcomes compared to MRI-positive cases.1 For TLE patients with normal hippocampal volume, however, previous
studies showed subtle volume changes in subregions of mesiotemporal lobe (MTL) structures
including the hippocampus, amygdala and entorhinal cortex.2 Here, for the first time, we proposed to use a surface-based
approach that allowed us to investigate metabolic changes in the subregions of MTL
structures for MRI-negative TLE patients and to what extent it is able to
explain seizure lateralization and surgical outcome.Methods
Dataset: Patients (N=58) with
either left (N=31) or right (N=27) lateralized MRI-negative TLE between the
ages of 14 and 70 were collated from the databases of University of California,
San Francisco and University of Alabama, Birmingham. Both 3D T1-MPRAGE MRI and [18F]
FDG-PET were acquired prior to temporal lobectomy and the Engel score was used
to assess patient outcome at 1-year post surgery.
Image
Processing: The hippocampus, entorhinal cortex and amygdala were each segmented
on T1-MPRAGE MRI using a multi-atlas and label fusion method.3 These segmentations were converted to a spherical harmonic
description (SPHARM), then sampled into triangulated surfaces using point-distribution
models (SPHARM-PDM).4 The PET intensity was normalized using the mean intensity of each
individual’s white-matter and CSF voxels, then was projected onto the SPHARM
surface. The asymmetry was calculated as the difference between the ipsilateral
and contralateral hemispheres divided by their sum.Results
We first investigated the
presence of asymmetries in the medial temporal lobe regions. Volumes were not
significantly asymmetric in the hippocampus, amygdala or entorhinal cortex, although
left TLE patients exhibited a slightly larger amygdala ipsilateral to the
epileptogenic region (Fig. 1a). There was significant hypometabolism on
FDG-PET in the hippocampus and amygdala for both left and right TLE patients
(p<0.05), i.e. lower metabolism in the MTL structures ipsilateral to the
epileptic focus compared to the contralateral side (Fig. 1b). Using SPHARM-PDM,
we analyzed the pattern of these asymmetries across cytoarchitectonic
subregions for each of the MTL structures (Fig. 2). The significant hypometabolism
in the MTL ipsilateral to the focus was mapped in the anterior to the
intermediate hippocampus, the intermediate entorhinal cortex and the
centro-medial and laterobasal amygdala. Finally, we investigated whether this
asymmetry differed between patients with good surgical outcome (Engel 1) and
poor outcome (Engel score 2-4) (Fig. 3). In patients with poor outcome,
metabolism was more interhemispherically symmetric in all 3 regions compared to
those with good outcome (Engel 1), although this did not reach statistical significance
p>0.2. In addition, there were no significant local associations between
asymmetry and outcome.Conclusions
Here, we investigated the
distribution of hypometabolism in the medial temporal lobe in MRI-negative TLE
patients. Asymmetry was highest in the anterior to intermediate hippocampus,
intermediate entorhinal cortex, lateral-baso and centro-medial amygdala. We
also found a trend of less asymmetric hypometabolism in patients with poor
surgical outcome. The nature of interhemispherically symmetric metabolism in
this group potentially suggests a more complicated seizure origin in these
types of patients and could relate to the lower likelihood of seizure freedom
after surgery. The absence of healthy controls is a primary limitation of the current
study, which complicates interpretation of the findings (e.g., whether there
exists bilateral hypometabolism or normal metabolism).Acknowledgements
This
study is supported by the National Institutes of Health grants
(P41EB015922) and the BrightFocus Foundation grant (A2019052S).References
1. Muhlhofer W, Tan YL, Mueller SG,
Knowlton R. MRI-negative temporal lobe epilepsy-What do we know? Epilepsia. 2017;58(5):727-742.
2. Bernhardt
BC, Hong SJ, Bernasconi A, Bernasconi N. Magnetic resonance imaging pattern
learning in temporal lobe epilepsy: classification and prognostics. Ann Neurol. 2015;77(3):436-446.
3. Wang
H, Suh JW, Das SR, Pluta JB, Craige C, Yushkevich PA. Multi-Atlas Segmentation
with Joint Label Fusion. IEEE Trans
Pattern Anal Mach Intell. 2013;35(3):611-623.
4. Styner
M, Oguz I, Xu S, Brechb¨uhler C, Pantazis D, Gerig G. Statistical Shape
Analysis of Brain Structures using SPHARM-PDM. MICCAI 2006 Opensource workshop;
2006.