Nao-Xin Huang1, Tian-Xiu Zou1, Zhongshuai Zhang2, and Hua-Jun Chen1
1Fujian Medical University Union Hospital, Fuzhou, China, 2SIEMENS Healthcare, Shanghai, China
Synopsis
White matter (WM) impairments have
been well documented in amyotrophic lateral sclerosis (ALS). This
study tested the potential of diffusion measurements in WM for identifying ALS
based on the support vector machine (SVM). In
the optimized SVM model, the FA values from the motor areas (including the bilateral
precentral gyrus and the corticospinal tract) and extra-motor areas (including right postcentral gyrus, left superior/inferior
longitudinal fasciculus) contributed mostly to classification. Our study
suggests the feasibility of ALS diagnosis based on SVM analysis and diffusion
measurements of WM. Future study with larger cohort is needed to validate the
generality of our results.
Introduction
As a cryptogenetic and fatal neurodegenerative disorder,
amyotrophic lateral sclerosis (ALS) often occurs in adults. This is a
heterogeneous disease, with difficulty in early diagnosis. From the onset of
symptoms to death, the average survival time is 3-5 years [1], and
Riluzole can only prolong the survival time of 2-3 months [2]. Therefore, early diagnosis of ALS and detection of its pathogenesis
are particularly important.
Diffusion tensor imaging (DTI) plays a key
role in investigating neuropathology of neurodegenerative disorders. The major
parameter of white matter (WM) fibers anisotropy is FA (a symbol of white
matter integrity). Several DTI studies have revealed that ALS patients showed
decreased FA in the corticospinal tract (CST) and extra-motor areas [3]. Actually, the decreased FA in the CST and corpus callosum is a
promising biomarker candidate to diagnose and evaluate ALS [4].
Support vector machine (SVM), a kind of
machine learning algorithm, has been widely used to investigate the
discriminative brain map for patients with psychiatric and neuropathic
disorders. A
prior resting-state functional magnetic resonance imaging study has used SVM to
identify ALS based on the functional connectivity measurement in brain networks
[5]. However, to our knowledge, there is no
research using SVM to discriminate ALS patients based on DTI measurement. Thus,
the objective of this study is to test the potential of diffusion measurements
in WM for identifying ALS based on the SVM learning method.Methods
Voxel-wise
fractional anisotropy (FA) values of the diffusion tensor images (DTI) were extracted
from 22 ALS patients and 26 healthy controls and served as discrimination
features. The disease severity of ALS was assessed based on the revised ALS
Functional Rating Scale (ALSFRS-R). The feature ranking and selection were
based on Fisher score. A linear kernel SVM algorithm was applied to build the
classification model, from which the classification performance was evaluated.
To promote the classifier generalization ability, a leave-one-out
cross-validation (LOOCV) strategy was then adopted.Results
When
taking the 2400~3400 ranked features as the optimal features, we achieved the
high classification accuracy of 83.33% (88.46% for sensitivity, 77.27% for
specificity, P=0.0001), with the area under receiver operating characteristic
curve of 0.862. The predicted function value was positively correlated with patients’
ALSFRS-R score (r=0.493, P=0.020). In the optimized SVM model, the FA values
from the following regions contributed mostly to classification: bilateral
corona radiate and precentral gyrus, right postcentral gyrus, right posterior
limb of internal capsule, left superior frontal gyrus, left angular gyrus, left
middle temporal gyrus, left middle occipital gyrus, bilateral midbrain,
bilateral pons and medulla, left frontal lobe, left inferior parietal lobule,
and right superior parietal lobule.Discussion
In the
present study, we combined DTI with SVM to classify ALS patients and healthy
controls. The high classification accuracy of 83.33% can be obtained in the
optimized SVM model. The FA values from both motor and extra-motor areas
contributed to classification, which indicated that ALS is a multiple system
neurodegenerative disease. Moreover, the predicted function value correlated
with ALS disease severity (indexed by ALSFRS-R score). The further ROC analysis
and permutation statistics further validate the reliability of our SVM classifier.
Consistent
with previous studies [6; 7], we found that the regions with decreased FA
involved the bilateral precentral gyrus and the CST (such as bilateral corona
radiate, right posterior of internal capsule, bilateral midbrain, bilateral
pons and medulla). The precentral gyrus is part of the primary
motor cortex (PMC), degenerative alterations of the PMC in ALS include
significantly decreased Betz cells and cortical thinning [8; 9]. The CST is the area of cortical control of
spinal cord activity, connecting the neurons in motor cortex and spinal cord [10]. Degeneration of the CST is a hallmark feature
of ALS [11]. To sum up, the damage of these motor regions
leads to motor neuron dysfunction (e.g. muscle weakness, loss of voluntary
control ) in ALS patients [12].
The regions with decreased FA also involved several the extra-motor
areas, such as right postcentral gyrus, left superior longitudinal fasciculus (SLF) (including left superior frontal gyrus, left
angular gyrus and left middle temporal gyrus) and left
inferior longitudinal fasciculus (ILF) (including left
middle temporal gyrus and left middle occipital gyrus), which consistent with
previous studies [13; 14]. For example, it has been demonstrated that the significant cortical thinning of the postcentral gyrus (namely primary
somatosensory cortex [15]) occurred in ALS. Also, the SLF, connecting frontal, parietal and temporal
lobes and playing a key role in language function [16], is disrupted in ALS [17; 18]. Meanwhile, the damage to the left ILF (this fiber primary associated
with visual processing, language/semantic function, and the regulation of
emotion [19]), has been revealed in ALS patients [20]. Therefore, the damage of these extra-motor regions (reflected by decreased
FA) may be associated with the non-motion dysfunctions in ALS, such as sensory
deficits, language dysfunction, behavioral and psychiatric abnormalities [21; 22].Conclusions
Our
results suggest the feasibility of ALS diagnosis based on SVM analysis and
diffusion measurements of WM. Future study with larger cohort is needed to
validate the generality of our results.Acknowledgements
This work was supported by grants from the National
Natural Science Foundation of China (No. 81501450), Fujian Provincial Science
Fund for Distinguished Young Scholars (No. 2018J06023), Fujian Provincial
Program for Distinguished Young Scholars (No. 2017B023), and Fujian Provincial
Health Commission Project for Scientific Research Talents (No. 2018-ZQN-28).References
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