Ji Won Bang1, Anna M Chen1,2, Carlos Parra1, Gadi Wollstein1, Joel S Schuman1, and Kevin Chan1,3
1Department of Ophthalmology, New York University, New York, NY, United States, 2Sackler Institute of Graduate Biomedical Sciences, New York University, New York, NY, United States, 3Department of Radiology, New York University, New York, NY, United States
Synopsis
Glaucoma is
considered to involve neurochemical alterations in the visual system. While the
role of excitotoxicity in glaucoma remains controversial, we showed that the
balance between glutamate, a main excitatory signal, and gamma-aminobutyric
acid (GABA), a main inhibitory signal, is involved in glaucoma pathogenesis. We
demonstrated that the visual cortex of glaucoma patients changes to an excitatory-dominant
state and that this change is driven by reduced GABA. Additionally, we showed
that visual field loss is associated with reduced N-acetyl-aspartate, a marker
for neuronal integrity. Taken together, these findings suggest that
neurochemical alterations may serve as informative markers for glaucoma.
Introduction
Glaucoma
is characterized by the progressive degeneration of the optic nerve and retinal
ganglion cells. While its pathogenesis is still unclear, accumulating studies
have shown that glaucoma involves alterations not only in the eye but also in
the central nervous system1. In particular, excitotoxicity due to
excessive amount of glutamate, a main excitatory neurotransmitter, has received
increasing attention in recent decades2-4. Previous studies have demonstrated
that injection of glutamate in the mammalian eye leads to severe degeneration
of ganglion cells5. However, enhanced glutamate was not observed in
a few studies involving humans and animals with glaucoma6,7. While
glutamate remains to be controversial, a recent study proposed that inhibitory
signals may be involved in glaucoma as well8. Based on these
findings, we investigated alterations to the excitatory-inhibitory balance in
the visual cortex in glaucoma. In addition, we examined how N-acetyl-aspartate
(NAA), a marker for neuronal integrity, is affected by glaucoma.Methods
10 glaucoma patients and 4 healthy
control subjects were scanned inside a 3-Tesla MRI scanner (Siemens MAGNETOM
Prisma) with a 20-channel head coil at New York University Center for
Biomedical Imaging. For anatomical localization, high-resolution T1-weighted MR
images were acquired using a multi-echo magnetization-prepared rapid gradient
echo sequence (256 slices, voxel size= 1×1×1 mm3). MRS for gamma-aminobutyric
acid (GABA) was obtained using a MEGA-PRESS sequence (TR/TE= 1500/68 ms) with
double-banded pulses. MRS for glutamate was obtained using a PRESS sequence (TR/TE=
3000/30 ms). The same single voxel (2.2×2.2×2.2 cm3) was placed
along the calcarine sulci in the most posterior part of the occipital lobe
bilaterally for both MEGA-PRESS and PRESS sequences (Figure 1).
Glutamate and GABA were separately
fitted by LCModel. We examined the reliability of quantification of each
metabolite using Cramer-Rao Lower bounds (CRLB). We normalized the amount of
GABA and glutamate using NAA values obtained from MEGA-PRESS, following LCModel
guidelines9. We calculated the ratio between excitatory and
inhibitory signals (E/I ratio) by dividing the amount of glutamate by that of
GABA.
Additionally, in order to examine
whether our standard metabolite for MEGA-PRESS normalization in LCModel (NAA)
was stable between groups, we normalized the amount of NAA with total creatine
(tCr; combined creatine and phosphocreatine) for PRESS for further evaluation. Results
We confirmed the
reliability of the quantification of GABA, glutamate, NAA, and tCr using CRLB.
The mean (±s.e.m.) CRLB was 8.786±0.300% for GABA, 9.214±0.939% for glutamate, 2.00±0.000% for NAA, and 2.714±0.304% for tCr. The E/I ratio in the visual
cortex was higher for the glaucoma group compared to the healthy control group
(Figure 3a; average enhancement= 16.51%;
t(12)= 1.897, P= 0.041, independent-samples t-test, 1-tailed). This difference
was driven by GABA (Figure 3c). GABA
was significantly lower for the glaucoma patients (Figure 3c; average reduction= 16.85%; t(12)= -3.105, P= 0.005,
independent-samples t-test, 1-tailed), whereas glutamate was comparable between
the two groups (Figure 3b; t(12)= -0.359,
P= 0.363, independent-samples t-test, 1-tailed). In addition to glutamate and
GABA, we further tested NAA’s stability in glaucoma, since this is the control
metabolite used in MEGA-PRESS. Although we did not find a significant
difference between groups, we observed a significant correlation between the
amount of NAA and the clinical Humphrey 24-2 visual field mean deviation score
(Figure 4; Pearson’s r= 0.746, P= 0.021). Discussion
Our
study shows that the E/I ratio becomes enhanced in glaucoma and that this
change is driven by GABA. GABA is known to play an important role in visual
processing. For example, GABAergic interneurons are involved in sharpening
feature selectivity in the primary visual cortex. Both optogenetic activation
of GABAergic interneurons and administration of GABA were shown to increase visual
feature selectivity10,11{Leventhal, 2003 #268}. These studies suggest that the visual
function of glaucoma patients might have been impaired by a significant
reduction of GABA.
Furthermore,
we did not find a significant change in glutamate. Although previous studies
showed that excessive glutamate may be involved in glaucoma, recent studies did
not observe enhanced glutamate6,7 and failed to ameliorate glaucoma
using memantine, which targets glutamate excitotoxicity12. Therefore,
more systematic studies are needed to understand the involvement of glutamate
in glaucoma.
In
addition to glutamate and GABA, we found that greater visual field loss is
associated with a larger reduction of NAA/tCr within glaucoma patients. It is
noteworthy that GABA/NAA is reduced even if NAA is also decreasing, which
further substantiates the reduction in GABA in the glaucomatous visual cortex.
While NAA has been implicated in neuronal health in many neurodegenerative
diseases13, tCr is presumably a stable metabolite. The changes in
GABA and NAA metabolisms, if verified in larger studies, may potentially help
guide more targeted interventions to glaucomatous neurodegeneration. Conclusion
Our
results show that neurochemical alterations are involved in glaucoma
pathogenesis. We demonstrate that the visual cortex adopts an
excitatory-dominant state in glaucoma and that this imbalance is driven by GABA
and not glutamate. Furthermore, we show that visual field loss is associated
with a reduction in NAA within glaucoma patients. Taken together, these
findings suggest that neurochemical alterations in MRS may serve as informative
markers for glaucoma. Future directions include investigating the interactions
between neurometabolites and the structure and function in the eyes and brains
of glaucoma. Acknowledgements
This work was
supported in part by the National Institutes of Health R01-EY028125 (Bethesda,
Maryland); BrightFocus Foundation G2013077, G2016030 and G2019103 (Clarksburg,
Maryland); Research to Prevent Blindness/Stavros Niarchos Foundation
International Research Collaborators Award (New York, New York), and an
unrestricted grant from Research to Prevent Blindness to NYU Langone Health Department
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