Santosh Kumar Bharti1, Brett Shannon2, Adam Levin2, Carol D Morris2, Laura Fayad3, and Zaver M Bhujwalla1,4
1Division of Cancer Imaging Research, Department of Radiology, Johns Hopkins University, School of Medicine, Baltimore, MD, United States, 2Department of Orthopaedic Surgery, Johns Hopkins University, School of Medicine, Baltimore, MD, United States, 3Musculoskeletal Radiology, Department of Radiology, Johns Hopkins University, School of Medicine, Baltimore, MD, United States, 4Department of Oncology, Johns Hopkins University, School of Medicine, Baltimore, MD, United States
Synopsis
Adipocytic tumors present a spectrum of
neoplastic disease including benign lipomas and their variants, atypical
lipomatous tumors, and malignant liposarcomas. Distinguishing areas of malignant
dedifferentiation from benign and atypical lipomatous tumors is a diagnostic
challenge due to overlapping magnetic resonance imaging characteristics, and
pre-operative diagnostic accuracy is poor. Here we have identified dramatic differences in
the metabolic profile of water-soluble and lipid extracts of adipocytic tumors,
suggesting that magnetic resonsance spectroscopy may have the potential to
improve diagnostic accuracy. Our data may also lead to potential metabolic
targets for treatment.
Introduction
Adipocytic tumors present a spectrum of
neoplastic disease including benign lipomas, atypical lipomatous tumors (ALTs),
and malignant liposarcomas. Liposarcomas are the most common soft tissue sarcoma,
accounting for approximately 20% of all adult soft tissue sarcomas [1]. Some liposarcomas are suspected to arise
through dedifferentiation of ALTs, a process that is not well understood. Pleomorphic liposarcomas are high-grade, aggressive tumors with high
metastatic potential and overall 5-year survival rate of 20-30% [2]. Distinguishing high-grade liposarcomas from
benign and atypical lipomatous tumors can be a diagnostic challenge with
implications for surgical and clinical management. The rate of misdiagnosis
is approximately 30–40% following radiological detection [3], and 7–17% on histological evaluation [4]. A major
objective of the present work is to develop metabolic determinants for adipocytic
tumor classification and to identify metabolic targets. Our data demonstrate
that high-resolution MRS may be used as an additional method for classification
and diagnosis of liposarcomas and benign lipomatous tumors. Methods
De-identified
human surgical samples were collected from the Department of Orthopaedic
Surgery, The Johns Hopkins University School of Medicine Baltimore, MD. One tissue specimen from a benign pleomorphic
lipoma and two tissue specimen from a pleomorphic liposarcoma were examined
using 1H and 31P MR spectroscopy. Tissue samples were snap frozen and stored at
-80°C until 1H MRS analysis. Dual phase solvent extraction was
performed on about 400 mg of tumor tissue. The aqueous phase was separated,
freeze dried, reconstituted in 600ul D2O PBS for NMR analysis.
Organic phase were dried under nitrogen stream and reconstituted in 600ul of
deuterated chloroform and methanol (2:1 ration). All MR spectra were acquired
on an Avance III 750 MHz (17.6T) Bruker NMR spectrometer equipped with a 5 mm
broad band inverse (BBI) probe. Metabolites were quantified using TSP and TMS
as internal standard in aqueous and lipid phases respectively. Spectral
acquisition, processing and quantification were performed using TOPSPIN 2.1
software. Results and Discussion
Representative
1H and 31P MR spectra of the aqueous phase of tissue
extracts obtained from a pleomorphic lipoma and liposarcoma are shown in Figure 1 and Figure 3. Metabolites were quantified and changes were reported in
term of percentage considering metabolites level in pleomorphic lipoma as 100%
(Figure 2). Depletion in branch
chain amino acids (-10%), tyrosine (-15%), phenylalanine (-25%), lactate
(-45%), pyruvate (-35-50%), acetate (-5-25%) and elevation in alanine (40%),
succinate (35-60%), glycine (400-500%), histidine (15-25%), glucose (100%),
glutamine (50%), glutamate (75%), and myo-inositol (300%) in pleomorphic
liposarcoma were observed. Variations in
the metabolic levels between two specimens obtained from the same tumor
indicate metabolic heterogeneity. 31P
MRS of the aqueous phase revealed high levels of phosphocholine in the pleomorphic
liposarcoma as compared to the lipoma (not detected). 1H and 31P MRS (representative
spectra in Figure 4 and Figure 5) analysis of the lipid phase, summarized in
Figure 4, identified depletion in lipid (-65%, CH3 peak at 0.9 ppm was
quantified) and an increase in phosphatidylethanolamine (75%) and
phosphatidylcholine (30%). Visible variations in TAG glycerol backbone
(4.2-4.3ppm) and -CH=CH- peaks from polyunsaturated fatty acids at 2.8ppm and
5.3ppm were also observed. We are currently
analyzing additional samples from pleomorphic lipoma and liposarcoma as well as
other types of sarcomas to expand this study. Our preliminary data support investigating
the use of 1H and 31P MRS of liposarcomas for
differentiation between subtypes.Acknowledgements
This work was supported by NIH R01 CA193365 and NIH P30CA06973References
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