A MatLab-based program is presented for predicting 13C NMR spectra and mass 13C isotopomer data of various tissue metabolites in a 13C tracer experiments. The program is useful for predicting changes in 13C multiplet patterns in NMR spectra and changes in mass isotopomer ratios in mass spectral data as a tissue responds to changes in flux of various substrates through completing pathways involving mitochondrial metabolism. The program tcaSIM2 (copies available free of charge) is also valuable for teaching metabolism and analysis of 13C NMR data and mass spec data in metabolic tracer experiments.
An example of how tcaSIM2 can be helpful in planning a 13C metabolic experiment. Consider an experimental plan to infuse 13C-enriched glucose into a glioma patient prior to surgery. A 13C NMR spectrum of the tumor extract removed during surgery could be used to evaluate the contribution of glucose to energy production and the extent of anaplerosis in tumor metabolism. One might initially ask, should I choose [1,6-13C]glucose or [U-13C]glucose for the experiment? The simulated 13C NMR spectra of glutamate ± flux of pyruvate into the TCA cycle via yPC (anaplerosis) are shown in Figure 2. These spectra show that the glutamate spectrum is sensitive to influx of labeled pyruvate into the TCA cycle via pyruvate carboxylase regardless of which labeled glucose is chosen for the experiment. However, they also demonstrate that the glutamate C2 resonance is quite sensitive to anaplerosis while the glutamate C4 resonance is less sensitive when [1,6-13C]glucose is chosen for the experiment. These results suggests that [U-13C]glucose may be a better choice for the experiment.
Comparison of experimental NMR spectra with those predicted by tcaSIM2. Figure 3 illustrates experimental 13C NMR data from a liver perfused with a cocktail of unlabeled substrates plus [U-13C]propionate with a goal of evaluating gluconeogenesis (GNG), total anaplerosis (yS plus yPC), and pyruvate cycling.2 A 13C isotopomer analysis of the multiplets appearing in the 13C NMR spectrum of glutamate isolated from liver and glucose isolated from perfusate indicated that total anaplerosis was 6-fold higher than TCA cycle flux, GNG was 4-fold higher that TCA cycle flux, and surprisingly, pyruvate cycling flux was 2-fold greater than TCA cycle flux. The spectra of glutamate and glucose predicted by tcaSIM2 using these flux parameters are shown next to the experimental spectra in Figure 3. The agreement is obvious.
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