Kun Qing1, Sahar Mansoor1, John P. Mugler, III1, Talissa A. Altes2, Nicholas J. Tustison1, Kai Ruppert3, Jaime F. Mata1, G.Wilson Miller1, Iulian C. Ruset4, F.William Hersman4,5, Joanne M. Cassani2, and Yun Michael Shim1
1University of Virginia, Charlottesville, VA, United States, 2University of Missouri School of Medicine, Columbia, MO, United States, 3University of Pennsylvania, Philadelphia, PA, United States, 4Xemed, LLC, Durham, NH, United States, 5University of New Hampshire, Durham, NH, United States
Synopsis
Existing literature describes
two distinctive phenotypes of chronic obstructive pulmonary disease (COPD): airway-predominant
chronic bronchitis and alveolar-predominant emphysema. In this study, based on results from pulmonary
function tests and computed tomography, we found a new mixed phenotype of COPD.
This mixed phenotype showed minimal emphysematous tissue destruction, but low diffusion
lung capacity (DLCO). Subsequent hyperpolarized xenon-129 MRI results indicated
that gas exchange to the pulmonary blood in lungs for this mixed phenotype was
significantly impaired as compared to controls and the classic COPD phenotypes.
Introduction
Existing literature indicates that cigarette smoking results in two distinctive phenotypes of chronic obstructive pulmonary disease (COPD): airway-predominant
chronic bronchitis (CB) and alveolar-predominant emphysema (EM) [1]. Routine
clinical tools, including pulmonary function tests (PFT) and computed tomography (CT) have their limitations for characterizing COPD. Hyperpolarized xenon-129 (Xe129) MRI, as a novel
imaging technique, provides a new way to measure lung physiology and
characterize COPD [2]. Purpose
The purpose of this study was to characterize COPD phenotypes and the associated pulmonary physiology using hyperpolarized xenon-129 (Xe129) MRI, and
compare the results with established clinical measurements.Methods
Thirteen
healthy and thirty-three COPD subjects were recruited for this study, and
underwent PFT and CT. COPD patients were phenotyped into three
groups by percent diffusion lung capacity (%DLCO) and CT: 1) emphysema
(EM): low %DLCO and high % of EM lung tissue on CT; 2) chronic bronchitis (CB):
high %DLCO and low % of EM lung tissue on CT; and 3) mixed indeterminate (IND) phenotype:
low %DLCO suggestive of EM but low EM lung tissue on CT. Xe129 MRI, including
ventilation imaging [3] and dissolved-phase imaging [2], was subsequently performed
to determine airflow limitation by measuring dead space ventilation (%VD)
[4] and alveolar gas exchange by measuring Xe129 gas diffused into interstitial
tissue (tissue/gas ratio) or into red blood cells (RBC; RBC/tissue ratio)
normalized by Xe129 gas in the airspaces [2]. One way ANOVA with Bonferroni
subgroup analysis was performed to compare the four groups of subjects. In
addition, to evaluate pulmonary perfusion in CB patients, two CB patients
underwent 3-D dynamic contrast enhanced (DCE) MRI. Maps of quantitative
perfusion parameters were extracted as described in [5], and compared with RBC/tissue
ratios.Results and Discussion
Moderately
negative correlation was found between the %DLCO and % of EM lung tissue
obtained by CT (R= -0.41, P= 0.017). Based on PFT and CT (Figure 1), patients
were classified into three phenotypes: 18% (6/33) EM phenotype; 21% (7/33) CB phenotype; and 61% (20/33) IND phenotype with low %DLCO, but
minimal emphysematous lung by CT. Airflow limitation (%FEV1 and Xe129 %VD)
was worse in the EM phenotype as
compared to all other groups (p<0.05) (Figure 2a, b). The IND phenotype
group had %FEV1 substantially overlapped with the CB group (p>0.05, Figure 2a),
and did not show significantly higher %VD than the control group (p>0.05,
Figure 2b). Similarly, no statistical differences were found in Xe129
tissue/gas ratios among the control, CB and the IND groups (p>0.05). Only
the EM group appeared to have lower tissue/gas ratios than all other groups
(p<0.05) (Figure 2c). However, the RBC/tissue ratios, measuring gas transfer
from the interstitium to the blood stream, were much lower in the IND phenotype
as compared to both EM and CB groups (p<0.05) (Figure 2d). Further, DCE MRI results from two patients of the
IND group (results from one patient shown in Figure 3) showed relatively normal
or high pulmonary blood flow/volume in regions with low RBC/tissue ratios
(white arrows, Figure 3). These results strongly support that the Xe129 gas was
able to diffuse into the interstitium but was unable to further transfer into
the RBCs in the IND group.Conclusion
In a mixed
phenotype of COPD (minimal emphysematous tissue destruction and impaired gas exchange)
as identified by PFT and CT, Xe129 MRI found that gas transfer from the tissue to
the blood was impaired but gas transfer from the airspaces to the tissue was
intact. Further investigation of this group is needed to identify whether it represents
pre-EM COPD patients at risk, or an entirely different phenotype with tissue
remodeling of the vasculature. Acknowledgements
This work was supported by NIH R01 HL109618 and R21 HL129112. References
[1] Izquierdo-Alonso, J.L. et al. Respir Med 107, 724-731.
[2] Qing, K., et al. J Magn Reson Imaging, 2014. 39(2): p. 346-59. [3] Qing K et al. Proc of
ISMRM 23 (2015): 1494. [4] Tustison N.J., et al. J Magn Reson Imaging, 2011. 34(4): p. 831-41 [5] Ohno, Y., et al. J
Magn Reson Imaging, 2004. 20(3): 353-365.