Russell Glenn1, Jens H Jensen1, Simon S Keller2, Joseph A Helpern1, and Leonardo Bonilha3
1Medical University of South Carolina, Charleston, SC, United States, 2University of Liverpool, Liverpool, United Kingdom, 3Charleston, SC, United States
Synopsis
Temporal
lobe epilepsy (TLE) is the most common form of medically refractory epilepsy
and is associated with focal brain abnormalities causing recurrent, unprovoked
seizures originating from the temporal lobe. However, cytoarchitectronic
changes can be detected outside of the temporal lobe and may be associated with
the clinical course of the disease. We implement a novel neuroimaging approach
which combines the strengths of diffusional kurtosis imaging and automated
fiber quantification for the non-invasive characterization of white matter
pathways and demonstrate its sensitivity to detect pathological alterations
associated with TLE. The proposed technique may provide further insights into
the clinicopathology of TLE.Background and Purpose
Temporal lobe epilepsy
(TLE) is associated with seizure onset and accompanying structural
abnormalities in the temporal lobe of the brain, with epileptogenesis often
being associated with mesial hippocampal sclerosis. However, a growing body of
evidence suggests that structural changes in TLE extend beyond the temporal lobe,
and the characterization of phenotypical abnormalities in TLE may provide
important insight into the largely variable clinical courses of the disorder. In
the present study, we implement a novel neuroimaging approach which combines
the strengths of diffusional kurtosis imaging (DKI)
1,2 and automated
fiber quantification (AFQ)
3 for characterizing pathological changes
in specific white matter (WM) pathways that constitute important conduits of
information to and from the temporal lobe.
Methods
Study Participants: A cohort of 32 adult subjects with left TLE (mean
age 44.8, SD 16.7; 22 females) and 36 age and gender matched controls (mean age 40.4, SD 11.6; 24 females) were
included in this study. All subjects were diagnosed with left TLE in
concordance with the diagnostic criteria proposed by the International League
Against Epilepsy (ILAE), including a comprehensive medical history and a full
neurological evaluation.
4 The subject population had varying disease
severity and included subjects with recently diagnosed, well-controlled, and
medication refractory TLE.
Image Acquisition: DKI datasets were
acquired with a 3T Magnetom Verio MRI scanner (Siemens Medical, Erlangen,
Germany) using a vendor-supplied, single-shot diffusion-weighted EPI sequence
with a twice refocused spin echo and a 12-channel head coil. The protocol
included 3 diffusion weightings of b = 0, 1000, and 2000 s/mm2, 30
isotropically distributed diffusion encoding directions, a total of 10 b = 0
images, TR / TE = 8500 / 98 ms, voxel dimensions = 3.0×3.0×3.0 mm3,
matrix size × number of slices = 74×74×40, and a parallel imaging factor = 2.
Image Analysis: DKI analysis included
the estimation of mean diffusivity (MD), fractional anisotropy (FA), mean
kurtosis (MK), axonal water fraction (AWF),
5 and DKI-derived
tractography
6,7 and was performed with diffusional kurtosis
estimator (https://www.nitrc.org/projects/dke/). DKI was incorporated into AFQ
software (https://github.com/jyeatman/AFQ) using fully automated in-house
scripts, including in-house algorithms to automatically segment the fornix. WM
tracts included were left and right fornix, parahippocampal white matter (PWM),
arcuate fasciculus (AF), inferior longitudinal fasciculus (ILF), uncinated
fasciculus (UF), and cingulum bundle. Statistical
Analysis: Along-the-tract profiles were created for each fiber group along
100 nodes and each tract was divided into 5 ROIs by averaging every 20
consecutive nodes. In all cases, tract node and ROI numbers increase closer to
or further anteriorly within the temporal lobe. Statistical analysis was
performed using repeated two-sample t-tests and significance was determined at
p < 0.05 after correcting for multiple comparisons with false discovery rate
(FDR) thresholding (n = 240 total comparisons). Effect size was calculated with
Cohen’s d parameter.
Results
Tract
profiles are summarized in Figures 1-2 and Tables 1-3. In general, MD tended to be
higher and FA, MK, and AWF tended to be lower in subjects with TLE; MK and AWF
showed more significant changes, larger effect sizes, and more expansive
group-wise differences compared to MD and FA; and the abnormal tract profiles
demonstrated a qualitative crescendo effect, increasing in significance into
the temporal lobe. Significant reductions in MK and AWF were found in the left
fornix and PHW in multiple ROIs in subjects relative to controls, consistent
with clinical observations of mesial hippocampal sclerosis in TLE. MK and AWF
also demonstrated significant changes in multiple ROIs in the left and right AF
and ILF indicating the presence of extrahippocampal pathology.
Discussion and Conclusion
By combining the
strengths of DKI and AFQ, we have implemented a novel diffusion MRI-based image
analysis technique, which can quantify microstructural abnormalities in
specific, functionally important WM fiber pathways. The along-the-tract
diffusion profiles were demonstrated to identify group-wise pathological
changes, with the largest effect sizes lateralizing to the left temporal lobe and
extending along the tracts beyond the left temporal lobe and including the
right side of the brain. By implementing a specific model of WM microstructure,
some of the observed changes may be attributed to neuronal loss via reduction
in AWF, which estimates the fraction of water that is confined inside WM axons.
Previous DTI studies average mean MD and FA across whole tracts, which may be
insensitive to regional tract alterations and overlook significant tissue
pathology. This is the first study to combine improved diffusion
characterization with DKI and along-the-tract profiles quantified by AFQ. This
technique may provide further insights into structural pathology underlying TLE
as well as other disorders affecting WM pathways.
Acknowledgements
This work was supported in part by National Institutes of Health
research grant T32GM008716 (to P. Halushka) and by the Litwin Foundation (to
J.A.H.).References
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