Elavarasan Subramani1, Chloe Najac1, Georgios Batsios1, Pavithra Viswanath1, Marina Radoul1, Anne Marie Gillespie1, Russell O Pieper2,3, and Sabrina M Ronen1,3
1Department of Radiology and Biomedical Imaging, University of California San Francisco, San Francisco, CA, United States, 2Department of Neurological Surgery, Helen Diller Research Center, University of California San Francisco, San Francisco, CA, United States, 3Brain Tumor Research Center, University of California San Francisco, San Francisco, CA, United States
Synopsis
The alkylating agent temozolomide (TMZ),
previously used only in the treatment of high-grade glioblastoma, is now being
considered for the treatment of low-grade glioma that are driven by mutations
in the cytosolic isocitrate dehydrogenase 1 (IDH1) gene. However, early detection
of response remains a challenge. 1H and hyperpolarized 13C
magnetic resonance spectroscopy-based metabolic profiling of cells genetically
engineered to express mutant IDH1 and treated with TMZ showed significant
alterations in metabolites majorly related to the tricarboxylic acid cycle, and
identified hyperpolarized 5-13C-glutamate metabolism as an indicator
of response. These findings hold potential for assessing response of IDH1
mutant cells to TMZ therapy.
Introduction
Gliomas
are the most common type of brain tumor in adults, representing 80% of primary
malignant tumors. Mutations in the cytosolic isocitrate dehydrogenase 1 (IDH1)
enzyme, which are present in up to 90% of primarily low-grade gliomas, lead to
a neomorphic activity of the enzyme that results in conversion of
α-ketoglutarate to the oncometabolite 2-hydroxyglutarate (2-HG).1,2 Mutant
IDH1 tumors are less aggressive than primary glioblastoma (GBM), but
nonetheless always recur and ultimately lead to patient death. To improve
patient survival, one therapeutic strategy is treatment with the alkylating
chemotherapeutic agent Temozolomide (TMZ), previously reserved for the
treatment of primary GBM.3 Though the treatment of IDH1 mutant
patients with TMZ improves survival,4,5 current imaging approaches
cannot identify early response to treatment. The goal of this study was,
therefore, to determine the value of magnetic resonance spectroscopy (MRS)-detectable
metabolic alterations as indicators of response to treatment. To this end, we investigated
a genetically engineered mutant IDH1 immortalized Normal Human Astrocyte
(NHA)-based cell model, and assessed the effects of TMZ on the cellular metabolic
profile (1H MRS combined
with chemometrics) and on specific metabolic pathways (hyperpolarized
and thermal equilibrium 13C MRS).Methods
NHAs
were genetically engineered to express mutant IDH1 (NHAIDHmut) and maintained
in culture as previously described.6,7 Cells were labelled with [1-13C]-glucose
and [3-13C]-glutamine and treated either with the IC50
value of TMZ (100 μM; N=5), or DMSO (1%; N=5) for 72 hours. 1H-MRS (1D
water presaturation ZGPR sequence, 90° FA, 3s TR, 256 acquisitions) and proton-decoupled
13C-MRS (30° FA, 3s TR, 2048 acquisitions) spectra of extracted
metabolites were acquired using a 500 MHz Bruker Avance spectrometer. 1H
MRS data was analyzed using SIMCA,8 first using a multivariate
principal component analysis (PCA), followed by partial least squares
discriminant analysis (PLS-DA). Correlation values were used to identify
metabolites altered with treatment. 1H and 13C MRS peaks were
manually integrated and quantified using Mnova7, integrals normalized to TSP
and to cell number and statistical significance of differences determined using
unpaired Student’s t-test (Graphpad). Pathway enrichment and topology analysis
of dysregulated metabolites was performed using MetPA.9 For hyperpolarized 13C-MRS studies, NHAIDHmut cells were encapsulated in
agarose and MRS studies performed in MR compatible cell perfusion system.9
Live cells were exposed to hyperpolarized 2-13C-pyruvate and
dynamic sets of 13C-MRS spectra recorded using 5°
FA and 3s TR over 300s to monitor the production of hyperpolarized 5-13C-glutamate.
Hyperpolarized glutamate signal was then quantified using
Mnova7 and normalized to pyruvate signal and cell number.Results and Discussion
As
expected, treatment of NHAIDHmut cells with the IC50 of TMZ resulted
in a 47.73±3.99% reduction in cell number. When inspecting the 1H
MRS spectra of control and treated cells, twenty-nine metabolites could be
identified using Human Metabolome DataBase and literature values. First, 1H
spectra of both groups were subjected to PCA to visualize the inherent
clustering of groups. The PCA score plot showed separation of TMZ-treated from
DMSO-treated control cells (Fig.1A). Further, improved separation between the
groups was obtained by PLS-DA (Fig.1B) and OPLS-DA (Fig.1C). Most significant
metabolites contributing to class separation were identified using correlation ≥0.6
(Fig.2A). A univariate analysis was then applied to the integral values of the
metabolites identified in this manner. Several metabolites were altered, most
notably an increase in glutamate and 2-HG were observed following treatment
(Fig.2B). Pathway enrichment and topology analysis of these metabolites showed
41 altered pathways in TMZ- treated cells. Based on their significance and
impact score, tricarboxylic acid (TCA) cycle and pyruvate metabolism were
identified as the most significant pathways altered following treatment (Fig.3).
To further assess whether the increase in
glutamate and 2-HG could be explained by an increase in TCA cycle flux, synthesis
of glutamate and 2-HG from 1-13C-glucose,
as well as from 3-13C-glutamine
were probed. Consistent with the
increase in total metabolite levels, both glucose- and glutamine-derived
glutamate (Fig.4A) and 2-HG (Fig.4B)
were increased in TMZ treated cells compared to controls, together
explaining the increase in total pools. Furthermore,
dynamically probing the metabolism of hyperpolarized 2-13C-pyruvate
revealed that build-up of 5-13C-glutamate, which is associated with
flux to the TCA cycle, was significantly higher in TMZ-treated cells as
compared to controls (Fig.5). Conclusion
Our
findings demonstrate that 1H MRS-detectable metabolomics combined
with hyperpolarized 5-13C-glutamate have the potential to serve as
biomarkers of low-grade glioma response to TMZ therapy. Further studies are
needed to confirm the generality of our findings in other mutant IDH1 models.
Nonetheless, these findings may help in enhancing currently available imaging methods
to improve the early detection of response to TMZ in low grade glioma.Acknowledgements
This work is supported by NIH R01CA197254 and NIH center grant P41EB013598. References
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