Helge Jörn Zöllner1,2, Georg Oeltzschner3,4, Markus Butz1, Markus S. Jördens5, Nur-Deniz Füllenbach5, Dieter Häussinger5, Hans-Jörg Wittsack2, and Alfons Schnitzler1
1Institute of Clinical Neuroscience and Medical Psychology, Medical Faculty, Heinrich Heine University Düsseldorf, Düsseldorf, Germany, 2Department of Diagnostic and Interventional Radiology, Medical Faculty, Heinrich Heine University Düsseldorf, Düsseldorf, Germany, 3Russell H. Morgan Department of Radiology and Radiological Science, The Johns Hopkins University School of Medicine, Baltimore, MD, United States, 4F.M. Kirby Research Center for Functional Brain Imaging, Kennedy Krieger Institute, Baltimore, MD, United States, 5Department of Gastroenterology, Hepatology and Infectiology, Medical Faculty, Heinrich Heine University Düsseldorf, Düsseldorf, Germany
Synopsis
Hepatic encephalopathy (HE) associated with elevated brain
ammonia levels. The detoxification of ammonia leads to regionally selective
alterations in several brain metabolites. The present study investigates these
neurotransmitter changes in HE patients in the GABAergic and glutamatergic
system. Using MEGA-PRESS, MR spectroscopy was performed in cerebellum,
thalamus, and motor cortex. Preliminary results unravel increased GABA levels
accompanied by elevated glutamine and reduced myo-Inositol in the cerebellum,
but an absence of GABA level changes in the two other regions. These initial
findings may lead to further explanation of cognitive and motor deficits in HE,
but need to be substantiated further.
Introduction
Hepatic
encephalopathy (HE) is associated with elevated ammonia leveles in the brain and the detoxification
of ammonia leads to regionally selective alterations in several brain
metabolites1. The
present study investigates these neurotransmitter changes in HE patients in the
GABAergic and glutamatergic system2,3, as well as myo-Inositol4,5, glutathione6,7, and aspartate8. The involvement of the motor system, thalamus, and cerebellum has
been demonstrated in human9 and rodent studies10 and is linked to cognitive impairment and motor deficits. The
present study investigates alterations in metabolite concentrations within the
human brain of HE patients, focusing on the cerebral neurotransmitter GABA and
glutamate, but also other HE related metabolites. Brain metabolite levels in
the cerebellum (CEREB), thalamus (THA), and motor cortex (M1) (Figure 1) were assessed with j-edited
proton magnetic resonance spectroscopy (MRS) to explore changes in brain
metabolism of HE patients.Methods
5 clinically well-characterized HE patients
and 7 healthy age-matched controls were investigated with J-edited MEGA-PRESS11 MRS (TE/TR = 68/1750 ms, NEX = 256, ‘ON’ pulse = 1.9 ppm, ‘OFF’ pulse = 7.5
ppm, CEREB: (25 mm)3, THA: (35 (LR) x 30 (AP) x 25 (HF)) mm3, M1: (30 mm)3) in this ongoing study. Voxel localization was based on an T1-weighted
anatomical scan. Critical flicker frequency (CFF) was recorded via a CFF goggle
(NevoLAB GmbH, Maierhöfen, Germany) in both groups, as it accounts for the
continuous nature of HE12.
The CFF is defined as the frequency at which the participant can distinguish a
flickering light source from a continuous one. The MR acquisition was performed
on a clinical 3T MRI (Siemens MAGNETOM Prisma, Siemens Healthcare AG, Erlangen,
Germany). GABA-to-creatine ratios were assessed with Gannet 3.013, whereas OFF spectra were processed with FID-A14 and evaluated using LCModel v6.315. Normal distributed data were tested with t-test, otherwise
the Mann-Whitney-U-test was used (both significance levels α = 0.05).
Tow-sided partial correlations with CFF and age as covariates were calculated,
again significance levels α = 0.05.Results
A sifnificant increase in GABA levels was detected in
the cerebellum (p < .05), whereas no GABA level changes were observed in the
THA and M1. An elevation of glutamine and a reduction in myo-Inositol was
visible in all regions of interest (all p < .01). In addition, aspartate
levels were increased within CEREB and M1 (both p < .05), as well as increased
glutathione levels in THA and M1 (both p < .05) (see Figure 1 & Figure 2).
CFF values (controls: 43.3 ± 2.2 Hz; HE: 36
± 1.7 Hz) were different (p < .05) between both groups. Negative correlations
between CFF and metabolite levels were found for glutamine (Gln) in CEREB,
Aspartate (Asp) in CEREB and M1, and for Glutathione (GSH) in M1. Positive
correlations between CFF and myo-Inositol (mI) were found in all regions (see Figure 3 & Figure 4).Discussion
Preliminary results point at a cerebellar
involvement in HE and are in line with the hyperammonemia rat model10. The increased GABAergic tone, which was accompanied by elevated
Gln and reduced mI, could be linked to detoxification of ammonia. Another
striking result is the link between Asp and HE within CEREB and M1. A
high-affinity uptake of aspartate was described in rats with HE8, but was to our knowledge not yet reported in human in vivo studies. Elevated GSH levels
within THA and M1 might be attributed to a oxidative stress response7. Further, patients – especially patients with minimal HE – should
be included to substantiate these findings.Conclusion
GABA j-edited MRS in cerebellum, thalamus,
and motor cortex unraveled increased GABAergic tone within the cerebellum.
Elevated Gln and mI depletion, which are typical for HE, were found in all
regions and were closely linked to CFF. In addition, increasing Asp level were
found in cerebellum and motor cortex. These findings underline the regionally
specific and continuous nature of HE.Acknowledgements
The authors would like to thank Erika Rädisch for the assistent during the MR measurements. Georg Oeltzschner received salary support from NIH R01EB016089, R01EB023963, R01MH106564, and R21AG060245. This study was supported by
the Sonderforschungsbereich (SFB) 974 (TP B07) of the Deutsche
Forschungsgemeinschaft (DFG).
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