Amol Pednekar1, Siddharth Jadhav1, Cory Noel1, and Prakash Masand1
1Texas Children's Hospital, Houston, TX, United States
Synopsis
Balanced
steady-state free precession imaging distinguishes the non-compacted left
ventricular (LV) myocardial trabeculation (NC) from compacted myocardium (C). However,
current diagnostic criterion (NC/C length ratio > 2.3) for left ventricular
non-compaction (LVNC) suffers from subjective variability and tends to
over-diagnose. Cumulative perimetric ratio (CPR) derived from epi and
endocardial contours routinely drawn for LV functional analysis provides
comprehensive measure of irregularity and extent of the LV trabeculations overcoming
the inherent morphologic variability from base to apex. CPR has a potential to
serve as a valuable biomarker for prominent trabeculations, complementary to NC/C
length and mass ratios.
PURPOSE
The
purpose of this study is to evaluate two-dimensional geometric marker viz. cumulative
perimetric ratio (CPR) to quantitate irregularity and extent of the left
ventricular (LV) myocardial trabecular structures in bright blood cine balanced
steady-state free precession MR images in a pediatric cohort. CPR index can be derived from epi and
endocardial contours typically drawn for LV functional analysis, complementary to the morphometric measures of non-compacted (NC) to compacted (c) myocardial length and mass ratios.INTRODUCTION
In
pediatric population it is highly important to differentiate patients with pathologic
left ventricular noncompaction (LVNC) who require regular surveillance and
likely activity restriction, from those who are within the range of physiologic
variant of hypertrabeculation and should not be activity restricted. Left
ventricular noncompaction (LVNC) has possible major cardiac clinical
manifestations such as congestive heart failure, arrhythmias, thromboembolism, and
sudden cardiac death [1, 2], thus it is critical to identify these patients
that require regular surveillance and likely activity restriction. Although MRI can reveal the
non-compacted trabeculation (NC) distinctly from compacted myocardium (C), the
current diagnostic criterion based on one dimensional measurements
(NC/C>2.3) suffers from subjective variability and tend to over-diagnose
left ventricular non-compaction (LVNC), especially in pediatric patients where
LV trabeculation varies on a continuous spectrum [3].METHODS
We retrospectively reviewed charts
of patients who underwent cardiac MRI between August 2014 and September 2018
for clinical indications of hyper trabeculation, LV non-compaction, as well as
patients with structurally normal cardiac anatomy such as anomalous coronary
origins, or Kawasaki disease. Patients with normal structural anatomy, preload,
and afterload conditions at the time of MRI were included in this study. Epi and endocardial contours (EC) were drawn on the
end-diastolic short-axis bSSFP images of the LV from mitral valve annulus to
apex (Fig. 1). These contours were used for automatic extraction of the
trabecular edges (T). The following quantitative indices were computed using
automated tool: 1) NC/C length ratio (LR) perpendicular to EC at each slice; 2)
MR = percent NC of (NC+C) for entire LV; and 4) perimetric ratio (PR = length
of T / perimeter of EC) for each slice. Global quantitative indices were
derived as: 1) maximum of LR (MLR) across all slices; 2) MR; and 4) CPR over
all slices. Combined criteria of MLR>2.3 and MR>35% was used to define patients
with prominent trabeculations with possible LVNC.RESULTS
A total of 80 patients (14.3±5.0 yrs) met the inclusion criteria. Representative
clinical images for the spectrum of degree of LV myocardial trabeculation with
the resultant CPR values are shown in Figure 2. The values for MLR (1.99±0.88, 0.5-4), MR (31.7±12.1,
13.2-55.6), and CPR (1.67±0.31, 1.20-2.41) increased with
degree of trabeculation as a continuous spectrum (Fig. 3). There is a
significant correlation between MR and MLR with correlation coefficient (r) of
0.85 (0.78-0.9). CPR has significant correlation with both MLR (0.73, 0.61-0.82)
and MR (0.82, 0.73-0.88). A total of 28 patients (15.3±5.5 yrs) met the criteria for prominent trabeculations.
Cut off value of CPR=1.6 yields 94% of area under the receiver operating
characteristics curve with 86% sensitivity and 89% specificity for
identification of patients with prominent trabeculations (Fig 4).DISCUSSION & LIMITATIONS
Cumulative perimetric ratio
captures the structural complexity (irregularity and sparsity) and extent of
the LV myocardial trabeculation. CPR provides comprehensive measure of irregularity
and extent of the LV trabeculations as it assimilates the inherent morphologic variation
in structural complexity of LV trabeculation from base to apex. Effects of structural complexity
and extent of myocardial trabeculation are amalgamated in CPR, thus it can
distinguish between non-compaction and hyper-trabeculation. CPR does not take
into account associated myocardial thinning which is crucial in settings of dilated
cardiomyopathy and LVNC. CONCLUSION
In
this study we described cumulative perimetric ratio as a novel index to summarily
quantify the degree of LV myocardial trabeculations. CPR derived from epi and endocardial contours routinely drawn for LV
functional analysis correlated strongly with morphometric measures of NC/C
length and mass ratios. CPR has a potential to serve as a valuable biomarker
for a quick quantitative assessment of degree of LV myocardial trabeculation. Furthermore,
CPR can serve as a potential indicator for further assessment for LVNC with other
established diagnostic tests.Acknowledgements
No acknowledgement found.References
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