Nivedita K Naresh1, Michal Schafer2, Lorna Browne1, Dunbar Ivy2, Dayna Zimmerman3, Vitaly Kheyfets4, Alexander J. Barker1,4, and Uyen Truong2
1Radiology, Children's Hospital Colorado, Aurora, CO, United States, 2Cardiology, Children's Hospital Colorado, Aurora, CO, United States, 3Pediatrics, Children's Hospital Colorado, Aurora, CO, United States, 4Bioengineering, University of Colorado Denver, Aurora, CO, United States
Synopsis
Pediatric
pulmonary arterial hypertension (PAH) is a significant cause of morbidity and
mortality. Acute
vasodilatory reactivity (AVR) using right heart catheterization is a necessary
component of a diagnostic PAH evaluation. The aim of this study was to
non-invasively evaluate AVR hemodynamic changes in pediatric patients with PAH
using 4D flow MRI. We
have shown that post-iNO treatment in pediatric PAH patients, peak velocity and peak wall shear stress were increased. Future studies in larger cohorts of PAH
pediatric patients are needed to comprehensively evaluate the effectiveness of
non-invasive AVR in comparison to gold standard right heart catheterization.
Introduction
Pediatric
pulmonary arterial hypertension (PAH) is a significant cause of morbidity and
mortality and is characterized by remodeling of the pulmonary vasculature,
ultimately leading to right heart failure. Acute vasodilatory reactivity (AVR)
using right heart catheterization is a necessary component of a diagnostic PAH
evaluation, which assesses disease severity, determines the route of therapy,
and is prognostic of survival (1,2). Given that 4D flow MRI can be used to
non-invasively evaluate complex hemodynamic changes in the pulmonary arteries
(3), and that parameters such as wall shear stress (WSS) have been shown to be
critical in vascular remodeling processes, the aim of this study was to
non-invasively evaluate AVR hemodynamic changes in pediatric patients with PAH
using 4D flow MRI.Methods
24 4D
flow MRI exams were performed in pediatric PAH patients (N = 12) before and after
inhalation of FiO2 1.0 and iNO 40ppm for 10 minutes on a 3T scanner (Ingenia,
Philips Medical Systems, Best, The Netherlands) using ECG gating and
respiratory navigator in a sagittal oblique 3D volume covering the mid-thorax.
Typical pulse sequence parameters included: TE/TR = 2.5-2.8/4.0-4.6 ms, flip
angle = 100, temporal resolution = 38-48 ms, VENC = 150 cm/s,
spatial resolution = 2.6 x 2.6 x 2.2-2.8 mm3. 4D flow MRI
post-processing was performed using a CVI42 platform (Version 5.9.1, Circle
Cardiovascular Imaging, Calgary, AB, Canada). Pre-processing included
correction for eddy current, noise and velocity aliasing. Planes were placed
perpendicular to the direction of flow in the main pulmonary artery (MPA),
right pulmonary artery (RPA) and left pulmonary artery (LPA). Blood flow
analyses for each plane included: stroke volume (SV), peak flow (Qmax),
peak velocity (Vmax), peak WSS (i.e. WSSmax)
and average wall shear stress (WSSavg). Pulmonary vascular
resistance index (PVRi) and mean pulmonary artery pressures (mPAP) were measured
during catheterization. Blood flow parameters, mPAP and PVRi pre and post NO
inhalation were compared using paired samples t-test.Results
Table
1 summarizes patient demographics and mPAP and PVRi measurements obtained
during catheterization. mPAP was reduced post-iNO (p<0.05 vs. pre-iNO) and
there was a trend towards reduced PVRi post-iNO (p=0.08). Table 2 summarizes
the various blood flow parameters obtained using 4D flow (mean ± standard deviation). Post-iNO, Vmax
and WSSmax were significantly increased in MPA (p <0.05
vs. pre-iNO).
There were no statistical differences in the other blood flow parameters due to
NO inhalation. Figure 1 shows an example velocity map measured pre- and
post-iNO where the peak velocity was increased post iNO. Figure 2 shows an
example wall shear stress map measured pre and post-iNO. Figure 3 shows box
plots summarizing the blood flow hemodynamics measured in MPA. Comparison of blood flow parameters derived from
4D flow with mPAP and PVRi revealed a positive correlation between mPAP and Qmax
both pre-iNO (R=0.6, p=0.044) and post-iNO treatment (R=0.8, p=0.004). There
was a trend towards a positive correlation between the change in PVRi and WSSavg
(R=0.5, p=0.06). There was no change in PA diameter post-iNO.Conclusions
Using
4D flow MRI, it has been previously shown that peak systolic velocity and wall
shear stress are lowered in PAH (3). Here, we investigate an intervention which
assess vascular reactivity (AVR). In pediatric PAH patients iNO appears to result
in significant changes in pulmonary flow parameters which can be measured using
the 4D flow MRI technique. Specifically, we have shown that post-iNO treatment
in pediatric PAH patients, Vmax and WSSmax were increased,
the latter coming back towards the value seen in previously described
normotensive controls. Ongoing recruitment of PAH pediatric patients is
occurring and pilot data from this prospective vascular reactivity 4D flow
study indicate the value of non-invasive AVR by MRI. Ongoing comparison to the gold
standard, invasive right heart catheterization, is occurring and we continue to
investigate the effect of vasodilators in modulating remodeling processes.Acknowledgements
No acknowledgement found.References
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